Congenital insensitivity to pain with anhidrosis: a case report.

نویسندگان

J. S. Kim

Y. J. Woo

G. M. Kim

C. J. Kim

J. S. Ma

T. J. Hwang

M. C. Lee

چکیده

We present a five-year-old girl with congenital insensitivity to pain with anhidrosis. A skeletal radiographic survey revealed several old fractures. Application of pilocarpine showed anhidrosis and nerve biopsy revealed a significant decrease in the number of myelinated and unmyelinated nerve fibres.

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